Abstract. VALEJO, Fernando Antonio Mourão; TIEZZI, Daniel Guimarães and NAI , Gisele Alborguetti. Abdominopelvic desmoid tumor. Rev. Bras. Ginecol. Obstet. El tumor desmoide (fibromatosis) es una entidad patológica extremadamente rara que se desarrolla de la fascia muscular y la aponeusorsis. Aunque sin. Tumor desmoide de la pared torácica. Visits. Desmoid tumors of the chest wall. Chest, 74 Desmoid tumors: a year radiotherapy experience.

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BalloGunar K. Microscopically the tumors are consisted of a dense collagenous matrix with highly differentiated fibroblasts and bundles of myofibroblasts.

All manuscripts are sent to peer-review and handled by the Editor or an Associate Editor from the team. Specifically, in general population they are rare and account for only 0.

In the present case imatinib seemed to have stopped progression of the tumor of about 6 months but then was rendered ineffective. Recognition and management of hereditary colorectal cancer syndromes. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. Skip to search form Desmoice to main content. General Regional Hospital George Papanikolaou.

Noncytotoxic drug therapy in children with unresectable desmoid tumors.

It usually appears as a mass body with symptomatology associated to location. Neoplasms Search for additional papers on this topic. A fine needle aspiration FNA cytology did not reveal any malignant cells, thus conservative local excision was performed.

Desomide review of literature.

The abdominal CT demonstrated a large heterogenous soft tissue intraabdominal mass measuring 16 x 8. ZagarsAlan PollackPeter W. Hormonal alterations also affect the etiopathogenia of these tumors as they can express estrogen and progesterone receptors 4.

Mandibular desmoid tumor . Case report Tumor desmoide mandibular

A WX mutation was found. Pre – dominance of beta – catenin mutations and beta – catenin dysregulation in esporadic aggressive fi bromatosis desmoid tumour. The syndrome is inherited by an autosomal dominant gene, the adenomatous polyposis coli APC gene. Treatment was once again changed to valdecoxib mg 1 x 1 and tamoxifen but the tumors continued growing.

Our case is the first case of a FAP patient bearing the WX mutation in whom multiple aggressive desmoid tumors developed which were resistant to all medical treatments, including NSAIDS, anti-estrogens and tyrosine kinase inhibitors.

Aristotle University of Thessaloniki. Plast Reconstr Surg Factros predicting local recurrence of desmoid tumours including proliferating cell nuclear antigen.

See more Access to any published article, in either language, is possible through the Journal web page as well as from Pubmed, Science Direct, and other international databases. Are you a health professional able desmiide prescribe or dispense drugs? Dequanter D, Gebhart M. Case report Patient is a woman who was diagnosed of attenuated familial adenomatous polyposis.

The barium enema demonstrated multiple polyps of the large bowel.

Tumor desmoide intraabdominal – ScienceDirect

Fibromatosis desmoid tumor of the breast mimicking a case of ipsilateral metachronous brest cancer. Four years after the diagnosis of desmoid tumor their started treatment with imatinib mg x 2 for 8 months.

Diagnosis is based on imaging test. Desmoid tumors dezmoide rare benign soft tissue tumors that don’t metastasize 1,7,8 but tend to invade locally and compress surrounding structures 1,7,8.

Palabras clave locally aggressive; breast mass; mesenchymal tumor; localmente agresivo; tumor de mama; tumores mesenquimales. Dear Editor, Desmoid tumors are solid masses of the fascia or of musculoaponeurotic tissue showing proliferation of well-differentiated fibroblasts or miofibroblasts. Previous article Next article. Neoplasms Search for additional papers on this topic.

Tumor desmoide sobre cicatriz de trocar tras colectomía laparoscópica

During that period the desmoid tumor remained stable in size. Case report A 28 old year old female first presented with reported rectal bleeding for about 6 months. Rev Esp Enferm Dig The exact etiology of desmoid tumors is poorly defined although several factors are acknowledged to be positively correlated with their development and growth 7,9. Showing of 23 references. Current ideas in desmoid tumours.

J Chir Paris ; 4: Trauma, and especially surgical, seems to be a potential initiating factor in desmoids tumor development 7,8,9. In the current patient despite the fact that the mutation was in codon the patient developed multiple aggressive desmoid tumors resistant to treatment.